Surgical treatment of a huge kaposiform hemangioendothelioma in the chest wall: A case study
نویسندگان
چکیده
Kaposiform hemangioendothelioma, a rare vascular pediatric tumor often associated with Kasabach-Merritt phenomenon, is characterized by severe thrombocytopenia and consumptive coagulopathy. Kaposiform hemangioendothelioma is a severe disease and may progress quickly, resulting in a high mortality. However, standard treatment regimens for Kasabach-Merritt phenomenon have not yet been established. We reported here an infant with a large congenital kaposiform hemangioendothelioma in his chest wall who responded extremely well to surgical excision.
منابع مشابه
Intestinal obstruction due to kaposiform hemangioendothelioma in a 1-month-old infant
RATIONALE Kaposiform hemangioendothelioma (KHE) is an aggressive vascular tumor, mainly occurring in infants and young children and previously reported cases were mainly cutaneous or visceral form. Intestinal kaposiform hemangioma was first reported in 2012. Intestinal type KHE showed better prognosis if the lesion was limited in the gastrointestinal tract and coagulopathy was not accompanied. ...
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